Comparison analysis of Abernethy malformation in children and adults

Abstract

Abstract: Objective To compare and analyze the characteristics of Abernethy malformation in adults and children. Methods Abernethy malformation patients from December 2020 to December 2024 were collected and analyzed. They were divided into child and adult groups, and the types of vascular malformations, clinical symptoms, diagnosis and treatment process, and disease outcomes of patients were compared and analyzed. Results A total of one case of Abernethy malformation was collected in both children and adults, both of which were type Ⅱ Abernethy malformations. Children with portal cavernous transformation were accompanied by splenorenal shunting, and the clinical manifestations of children were prone to febrile seizures. Adult patients with hepatic encephalopathy were treated with medication, and the condition was stable. Conclusion Conservative drug treatment can achieve good clinical results in patients with mild Abernethy malformation symptoms.

Key words: Abernethy malformation, Hepatic encephalopathy, Computed tomography angiography

WANG Qian, WANG Wei-wei, REN Hong-wei, ZHAO Sheng-xiang, LI wei. Comparison analysis of Abernethy malformation in children and adults[J]. Chinese Hepatolgy, 2025, 30(10): 1410-1413.

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