关键词: 布加综合征, 临床分析, 诊治经验

Abstract: Objective To analyze the clinical features, experience in diagnosis and treatment of Budd-Chiari syndrome (BCS), and to provide reference for clinical diagnosis and treatment.Methods The clinical data of 9 patients with Budd-Chiari syndrome in Shuguang Hospital affiliated to Shanghai University of traditional Chinese Medicine from 2017 to 2021 were collected, and their main clinical manifestations, liver function, imaging results and misdiagnosis situation were summarized.Results The main clinical manifestations of 9 patients with BCS were hepatomegaly/splenomegaly, esophageal varices, abdominal distension, ascites, costal pain, abdominal wall varices, upper gastrointestinal bleeding and distending pain in hypochondrium; no obvious abnormality of liver function; imaging examination showed that the patients with inferior vena cava obstruction/stenosis were dominant; the clinical misdiagnosis rate was high (77.8%) and was often misdiagnosed as liver cirrhosis.Conclusion The clinical manifestations of BCS are complex and changeable, and it is easy to be missed and misdiagnosed; Besides vascular imaging examination, liver biopsy pathology also has important value; good effect can be obtained in the treatment of this disease when combined with the traditional Chinese medicine of invigorating qi and activating blood.

Key words: Budd-Chiari syndrome, Clinical analysis, Experience in diagnosis and treatment