关键词: 肝脏上皮样血管平滑肌脂肪瘤, 磁共振, 体层摄影术, 肿瘤标志物

Abstract: Objective To analyze the clinical and MR imaging features of 19 patients with hepatic epithelioid angiomyolipoma (HEAML). Methods The clinical data including sex, age, clinical signs, laboratory tests and imaging findings of 19 patients with pathological data of biopsy or surgery who were admitted to the fifth medical centre of PLA general hospital from October 2013 to October 2023 were summarized and analyzed. Results The clinical manifestations of these 19 HEAML patients were mainly focal liver lesions found by physical examination, symptoms of abdominal pain or distension, nausea and poor appetite. Among the 19 patients, 3 patients were positive for hepatitis B viral markers and 15 patients were negative for tumor markers. On the MR images, 18 patients had single lesions with an average diameter of about 5.4cm,14 patients were diagnosed with liver cancer, 16 patients had obvious enhancement in liver lesions, and 6 patients had false capsule enhancement in the delayed phase. Conclusion HEAML was predisposed to middle-aged women. It was mostly discovered by physical examination. Most of the patients have normal laboratory test results. Only individual patient has mild abnormal tumor markers. The imaging features were usually single rich-blood liver lesions. The strengthening mode was early obvious strengthening. False capsule enhancement in the delayed period can be found in part of the patients. The imaging features has certain guiding significance for the diagnosis of HEAML. The diagnosis of HEAML may be confirmed by a combination of clinical data with typical pathological results.

Key words: liver, magnetic resonance imaging, tomography, epithelioid angiomyolipoma