门静脉性肺动脉高压研究进展

摘要/Abstract

摘要： 门静脉性肺动脉高压是门静脉高压患者一种罕见但严重的并发症,以肺动脉压升高和肺血管阻力增加为特征,多见于肝硬化患者,其发病率低,临床表现不明显,主要依赖于有创检查确诊,临床上难以诊断,且该病的药物治疗效果不佳,严重的肺动脉高压可显著增加患者病死率,预后差。因此,该病的早期诊断和治疗尤为关键。本文结合近期文献,系统综述该病的流行病学、发病机制、危险因素、临床特征、诊断及治疗进展,旨在提高对该疾病的认识,并提出未来研究方向。

关键词: 高血压, 肝硬化, 门静脉, 肺动脉高压

朱娜, 戴光荣. 门静脉性肺动脉高压研究进展[J]. 肝脏, 2026, 31(3): 453-457.

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