肝脏 ›› 2025, Vol. 30 ›› Issue (10): 1410-1413.

• 其他肝病 • 上一篇    下一篇

儿童Abernethy畸形和成人Abernethy畸形对比分析

王倩, 王巍巍, 任洪伟, 赵胜祥, 李伟   

  1. 100000 北京 武警北京市总队医院医学影像科(王倩,李伟);102004 北京北亚骨科医院放射科(王巍巍,赵胜祥);100036 北京 解放军总医院第五医学中心放射诊断科(任洪伟)
  • 收稿日期:2025-02-08 出版日期:2025-10-31 发布日期:2025-12-16
  • 通讯作者: 李伟,Email:m13810149945@163.com

Comparison analysis of Abernethy malformation in children and adults

WANG Qian1, WANG Wei-wei2, REN Hong-wei3, ZHAO Sheng-xiang2, LI wei1   

  1. 1. Department of Medical Imaging,Beijing Armed Police Corps Hospital of PLA, Beijing 100000,China;
    2. Department of Radiology,Beijing Bei Ya Orthopedic Hospital,Beijing 102004,China;
    3. Department of Radiology,the Fifth Medical Center of the PLA General Hospital,Beijing 100036,China
  • Received:2025-02-08 Online:2025-10-31 Published:2025-12-16
  • Contact: LI Wei,Email:m13810149945@163.com

摘要: 目的 对比分析Abernethy畸形成人与儿童病例特征。方法 收集整理2020年12月至2024年12月Abernethy畸形患者,分为儿童和成人组,对比分析患者血管畸形类型、临床症状、诊疗经过及病情转归。结果 共收集到儿童和成人Abernethy畸形患者各1例,均为Ⅱ型 Abernethy畸形,儿童患者伴门静脉海绵样变,两者均伴发脾肾分流,儿童患者临床表现为易高热惊厥,成年患者表现为肝性脑病,患者均采取药物治疗,病情稳定。结论 Abernethy畸形儿童和成人症状轻微者经药物保守治疗均可取得较好临床效果。

关键词: Abernethy畸形, 肝性脑病, CTA

Abstract: Objective To compare and analyze the characteristics of Abernethy malformation in adults and children. Methods Abernethy malformation patients from December 2020 to December 2024 were collected and analyzed. They were divided into child and adult groups, and the types of vascular malformations, clinical symptoms, diagnosis and treatment process, and disease outcomes of patients were compared and analyzed. Results A total of one case of Abernethy malformation was collected in both children and adults, both of which were type Ⅱ Abernethy malformations. Children with portal cavernous transformation were accompanied by splenorenal shunting, and the clinical manifestations of children were prone to febrile seizures. Adult patients with hepatic encephalopathy were treated with medication, and the condition was stable. Conclusion Conservative drug treatment can achieve good clinical results in patients with mild Abernethy malformation symptoms.

Key words: Abernethy malformation, Hepatic encephalopathy, Computed tomography angiography